ManuScript Details
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Paper Id:
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IJCIRAS1694
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Title:
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STROMAL TUMOR IN VON-RECKLINGHAUSEN DISEASE
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| Published in: |
International Journal Of Creative and Innovative Research In All Studies |
| Publisher: |
IJCIRAS |
| ISSN: |
2581-5334 |
| Volume / Issue: |
Volume 3 Issue 6 |
| Pages: |
7
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| Published On: |
11/23/2020 9:37:58 PM (MM/dd/yyyy) |
| PDF Url: |
http://www.ijciras.com/PublishedPaper/IJCIRAS1694.pdf |
Main Author Details
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Name:
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BENSETTI HOUARI Amina Karima |
| Institute: |
university of medecine |
Co - Author Details
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Author Institute |
Abstract
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Research Area:
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General surgery |
| KeyWord: |
stromal tumor, neurofibromatosis, occlusion |
| Abstract: |
Summary :
The association of digestive stromal tumors and Von Recklinghausen's disease is of the order of 25% of cases in autoptic studies and only 5% with clinical manifestation; our observation focused on a particular mode of revelation in a table of acute intestinal obstruction, remains a diagnosis to be evoked given the frequency of the association and to be taken into consideration given the potential of malignancy of stromal tumors.
Observation:
63-year-old man with a history of VON RECKLINGHAUSEN's disease, treated for a subocclusive syndrome, Clinical examination found multiple neurofibromas disseminated on all the trunk with coffee milk spots.
Palpation perceives a sub-umbilical mass of imprecise limits, Morphological examination (CT, ECHO): Grelic tissue formation measuring 92mm × 52mm heterogeneous with grelic distension upstream; Normal tumor markers (CA 19 9, ACE); Normal rectosgmoidoscopy up to 55cm from the anal margin, the diagnosis of a secondary localization of a neurofibroma was suspected, a laparotomy is indicated due to the table of occlusion on an obstructive gel mass, exploration after laborious viscerolysis highlights evidence of two formations of ileal seat, one voluminous extraluminal one of 100 × 40mm invading the sigmoid colon as well as a second location of 20mm surgical resection removing the masses with a safety margin of 05cm with double anastomosis, post-suites The anatomopathological study returned in favor of a low-grade spindle-shaped cell tumor with dual localization evoking a GIST or others supplemented by immunohistochemistry confirming the low-grade stromal nature. Patient referred to oncology for further treatment. His follow-up patient did not present with tumor recurrence until the last CT scan in May 2015.
Conclusion: in a patient with Recklinghausen's disease with an occlusive syndrome, do not rule out the possibility of association with stromal tumors given the frequency of the association of Recklinghausen, GIST with multiple characters.
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Citations
Copy and paste a formatted citation or use one of the links to import into a bibliography manager and reference.
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IEEE
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BENSETTI HOUARI Amina Karima , "STROMAL TUMOR IN VON-RECKLINGHAUSEN DISEASE", International Journal Of Creative and Innovative Research In All Studies,
vol. 3, no. 6, pp. 21-27, 2020.
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MLA
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BENSETTI HOUARI Amina Karima "STROMAL TUMOR IN VON-RECKLINGHAUSEN DISEASE." International Journal Of Creative and Innovative Research In All Studies,
vol 3, no. 6, 2020, pp. 21-27.
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APA
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BENSETTI HOUARI Amina Karima (2020). STROMAL TUMOR IN VON-RECKLINGHAUSEN DISEASE. International Journal Of Creative and Innovative Research In All Studies,
3(6), 21-27.
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STROMAL TUMOR IN VON-RECKLINGHAUSEN DISEASE
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